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Middle East Journal of Digestive Diseases، جلد ۱۶، شماره ۳، صفحات ۱۹۶-۱۹۹
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عنوان انگلیسی Systemic Amyloidosis Presenting as Budd-Chiari Syndrome: a Case Report
چکیده انگلیسی مقاله Budd-Chiari syndrome (BCS) is characterized by hepatic venous outflow tract obstruction and is commonly associated with an underlying hypercoagulable state. Systemic amyloidosis is a disorder characterized by systemic deposition of misfolded proteins leading to end organ damage. Amyloidosis is commonly associated with coagulation abnormalities, mainly leading to increased bleeding diathesis. Here, we report a case of amyloid light chain (AL) amyloidosis presenting as BCS.  A 40-year-old man presented with abdominal distension along with anorexia and weight loss. On evaluation, he had severe hypoalbuminemia, raised alkaline phosphatase, and non-visualization of hepatic veins on abdominal imaging. Further evaluation confirmed the diagnosis of AL amyloidosis with renal, cardiac, and hepatic involvement. AL amyloidosis rarely can present with BCS. A high index of suspicion is needed as symptoms can be variable and non-specific.
کلیدواژه‌های انگلیسی مقاله Budd-Chiari syndrome,Systemic amyloidosis,Hypercoagulability,infilterative liver disease
نویسندگان مقاله | Naman Lodha
Department of General Medicine, All India Institute of Medical Sciences, Jodhpur


| Samarth Bhat K S
Department of Gastroenterology, All India Institute of Medical Sciences, Jodhpur


| Kartikeya Mathur
Department of Gastroenterology, All India Institute of Medical Sciences, Jodhpur


| Satyam Kumar Singh
Department of Diagnostic and Interventional Radiology, All India Institute of Medical Sciences, Jodhpur


| Rengarajan Rajagopal
Department of Pathology and Lab Medicine, All India Institute of Medical Sciences, Jodhpur


| Vikrant Verma
Department of Gastroenterology, All India Institute of Medical Sciences, Jodhpur


| Chhagan Lal Birda
Department of Gastroenterology, All India Institute of Medical Sciences, Jodhpur


| Ashish Agarwal


نشانی اینترنتی http://mejdd.org/index.php/mejdd/article/view/2998
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زبان مقاله منتشر شده en
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نوع مقاله منتشر شده Case Report
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